Spindle cell vulvar hemangiomatosis associated with enchondromatosis: a rare variant of Maffucci's syndrome

Int J Gynecol Pathol. 2004 Jan;23(1):68-70. doi: 10.1097/01.pgp.0000101149.01933.f7.


Spindle cell hemangioma is a rare vascular tumor that most frequently involves the distal extremities, especially the hand. We report a case of spindle cell hemangiomatosis of the vulva in an 18-year-old woman with Maffucci's syndrome, the first report of such a case, to the best of our knowledge. The vascular lesions, present from the age of 2, were located in the right olecranon, the third left toe, and the vulva. Spindle cell hemangiomas are either benign neoplasms or hamartomatous malformations.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Enchondromatosis / pathology*
  • Female
  • Hemangioma / pathology*
  • Humans
  • Vulvar Neoplasms / pathology*