Abstract
Cutaneous polyarteritis-nodosa-like lesions are rarely described in Behcet's disease. We report a case of recurrent cutaneous polyarteritis-nodosa-like (C-PAN-like) lesions in Behcet's disease with multiple deep vein thromboses as part of systemic vasculitis. The mucocutaneous manifestations responded to prednisolone; however, C-PAN-like lesions were refractory and responded to oral cyclosporine. We conclude that C-PAN-like lesions may be marker of severe disease and require intense immunosuppressive therapy.
MeSH terms
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Adolescent
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Anticoagulants / therapeutic use
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Azathioprine / therapeutic use
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Behcet Syndrome / complications*
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Behcet Syndrome / drug therapy
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Colchicine / therapeutic use
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Cyclosporine / therapeutic use*
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Heparin / therapeutic use
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Humans
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Immunosuppressive Agents / therapeutic use*
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Male
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Methotrexate / therapeutic use
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Polyarteritis Nodosa / complications*
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Polyarteritis Nodosa / drug therapy
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Prednisone / therapeutic use
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Thrombophlebitis / etiology
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Warfarin / therapeutic use
Substances
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Anticoagulants
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Immunosuppressive Agents
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Warfarin
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Cyclosporine
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Heparin
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Azathioprine
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Colchicine
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Prednisone
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Methotrexate