Bannayan-Zonana syndrome associated with lipomas, hemangiomas, and lymphangiomas

J Pediatr Surg. 1992 Jun;27(6):722-3. doi: 10.1016/s0022-3468(05)80100-9.


Bannayan-Zonana syndrome is a rare disorder characterized by macrocephaly and multiple soft tissue and visceral hamartomas. This report presents a sporadic patient with macrocephaly, lipomas, hemangiomas, and lymphangiomas who died of cardiac and respiratory failure due to progressive cervicomediastinal arteriovenous fistulous hemangiomas at the age of 9 years.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple*
  • Arteriovenous Fistula
  • Female
  • Hamartoma*
  • Head / abnormalities*
  • Hemangioma
  • Humans
  • Infant
  • Lipoma
  • Lymphangioma
  • Neoplasms, Multiple Primary*
  • Prognosis
  • Soft Tissue Neoplasms*
  • Syndrome