Abstract
A child is described who had the signs of autoimmune lymphoproliferative syndrome from an early age and later developed a blistering dermatosis that was shown to be childhood linear IgA disease.
MeSH terms
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Apoptosis
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Autoimmune Diseases / complications*
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Autoimmune Diseases / immunology
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Blister / complications
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Blister / immunology
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Humans
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Immunoglobulin A / immunology*
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Infant
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Lymphoproliferative Disorders / complications*
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Lymphoproliferative Disorders / immunology
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Male
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Skin Diseases / complications*
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Skin Diseases / immunology