Number of Edb motor units estimated using an adapted multiple point stimulation method: normal values and longitudinal studies in ALS and peripheral neuropathies

Clin Neurophysiol. 2004 Mar;115(3):557-63. doi: 10.1016/j.clinph.2003.11.001.

Abstract

Objective: To validate the adapted multiple point stimulation (AMPS) method to estimate the number of motor units (MUNE) from the extensor digitorum brevis (Edb) muscle.

Methods: Twenty controls (10 young and 10 old) were examined on both sides and 10 patients with amyotrophic lateral sclerosis (ALS) and 5 with acute peripheral neuropathy (PN) were examined longitudinally on one side during a series of repeated electrophysiological sessions.

Results: In the controls, the median MUNE and size of the motor unit action potentials (S-MUAPs) were found to be age-related (411 and 70 microVms in the young group; 164 and 142 microVms in the old group; P < 0.01), with a coefficient of variation of MUNE values of 27% and 20%, respectively. In the ALS group, the median MUNE value at diagnosis was 31 (P < 0.05 vs. controls), and during a mean follow-up period of 11.5 months a continuous decrease in the MUNE value was seen, together with an initial increase, followed by a later decrease in 4 cases, in S-MUAP size. In the PN group, the MUNE value was initially similar to that in controls, but then decreased, accompanied by an increase in S-MUAP size, and then showed a progressive increase, together with a decrease in S-MUAP size.

Conclusions: AMPS, a MUNE method developed in the upper extremity, also appears to be a useful procedure for quantifying changes in the MUNE value in the Edb muscle without specific software in order to study age-related changes or changes in patients with ALS or PN.

Publication types

  • Validation Study

MeSH terms

  • Acute Disease
  • Adult
  • Aged
  • Amyotrophic Lateral Sclerosis / physiopathology*
  • Case-Control Studies
  • Cell Count
  • Electric Stimulation / methods
  • Electromyography / methods*
  • Female
  • Humans
  • Longitudinal Studies
  • Male
  • Middle Aged
  • Motor Neurons*
  • Muscle, Skeletal / innervation*
  • Muscle, Skeletal / physiopathology
  • Neuromuscular Junction / physiopathology*
  • Peripheral Nervous System Diseases / physiopathology*
  • Toes