Bulbous urethra involved in perineal extraskeletal myxoid chondrosarcoma in a child

Int J Urol. 2004 Jun;11(6):436-9. doi: 10.1111/j.1442-2042.2004.00811.x.


Extraskeletal myxoid chondrosarcoma is a rare soft-tissue sarcoma that usually occurs in deep soft tissues, especially those of the proximal extremities and limb girdles, but is rare in children. We present an unusual case of a tumor arising in the perineum and involving the bulbous urethra in a 21-month-old boy. The patient was treated with surgical excision and urethroplasty followed by combination chemotherapy.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Chondrosarcoma / pathology*
  • Chondrosarcoma / therapy
  • Humans
  • Infant
  • Male
  • Perineum / pathology*
  • Soft Tissue Neoplasms / pathology*
  • Soft Tissue Neoplasms / therapy
  • Urethral Neoplasms / pathology*
  • Urethral Neoplasms / therapy