Fibrosing mediastinitis causing rapidly progressive dyspnea, pulmonary edema and death in a 16 yr old male

Monaldi Arch Chest Dis. 2004 Apr-Jun;61(2):124-7. doi: 10.4081/monaldi.2004.711.

Abstract

Idiopathic fibrosing mediastinitis is a rare entity involving more severely the more compliant structures within the mediastinum. In this report a rare case of simultaneous involvement of both the superior vena cava (SVC) and pulmonary veins is described in a 16--year old male with progressive dyspnea on exertion, cough and a three months' history of blood--tinged sputum. Physical examination and imaging studies revealed signs of pulmonary venous hypertension (PVH) and SVC stenosis. Fibrosing mediastinitis was confirmed by multiple biopsy samples.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Dyspnea / etiology*
  • Fatal Outcome
  • Fibrosis
  • Humans
  • Hypertension, Pulmonary / etiology
  • Male
  • Mediastinitis / complications*
  • Pulmonary Edema / diagnostic imaging
  • Pulmonary Edema / etiology*
  • Superior Vena Cava Syndrome / etiology
  • Tomography, X-Ray Computed