"Craniofacial and dental manifestations of a case of Proteus syndrome"

J Indian Soc Pedod Prev Dent. 2004 Sep;22(3):154-7.


Proteus syndrome, which is a reference to the ancient Greek god Proteus, the Polymorphous, was called to the attention of pediatricians. Recognition of this syndrome has been difficult because of the variability of the syndrome's manifestations and because of its rarity. We describe a rare case of Proteus syndrome and we discuss its differential diagnosis. Our case presents with hemi facial hypertrophy, scrotal tongue, enamel hyperplasia as well as differential in the size of the dentition on both sides of the arch.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Craniofacial Abnormalities / etiology*
  • Early Diagnosis
  • Facial Asymmetry / etiology
  • Humans
  • Male
  • Odontometry
  • Proteus Syndrome / complications*
  • Proteus Syndrome / diagnosis
  • Tongue / abnormalities
  • Tooth Abnormalities / etiology*