Assessment of adrenal endocrine function in Asian thalassemics

Indian Pediatr. 2005 Jan;42(1):31-5.

Abstract

Adrenal endocrine function was assessed in a cohort of 20 patients, between 10 and 20 years of age, with transfusion dependent beta thalassemia. Cortisol levels were assayed before and after ACTH stimulation with 1 micrograms and 250 micrograms. Adrenal dysfunction was defined as a basal cortisol of greater than 400 nmol/L and/or peak cortisol levels of greater than 500 nmol/L. Overall, 9 patients (45 %) had in vitro evidence of adrenal dysfunction. A statistical significant correlation (r=0.4308; P < 0.05), between wasting and the basal cortisol level, was observed. Similarly, there was correlation between the number of transfusions received and growth failure (r=0.4774;P < 0.05). In comparison to the involvement of other endocrine axes in polytransfused thalassemics, the adrenal endocrine function abnormalities are minor and clinically of little consequence. The observations, albeit, in a small cohort of thalassemics, stress the need for an annual estimation of basal cortisol level, especially in patients with wasting.

Publication types

  • Comparative Study

MeSH terms

  • Adolescent
  • Adrenal Insufficiency / metabolism
  • Adrenal Insufficiency / physiopathology*
  • Adult
  • Asian People
  • Child
  • Endocrine System / metabolism
  • Endocrine System / physiopathology*
  • Female
  • Humans
  • Hydrocortisone*
  • Iron / adverse effects*
  • Male
  • Risk Assessment
  • beta-Thalassemia / metabolism
  • beta-Thalassemia / physiopathology*

Substances

  • Iron
  • Hydrocortisone