Bednar tumor

Saudi Med J. 2004 Dec;25(12):2016-7.

Abstract

Pigmented dermatofibrosarcoma protuberance DSFP, also known as Bednar tumor or formerly known as pigmented storiform neurofibroma is a rare variant of DSFP. Bednar first described it in 1957. The histology is striking because of the presence of multipolar pigment laden dendritic cells scattered among spindle shaped cells with a storiform pattern, the latter being characteristic of DSFP. The spindle cells are positive for CD34, and Vimentin and negative for S100. The pigment represents melanin. We describe such a tumor because of its rarity and very striking microscopic appearance.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Biomarkers, Tumor / analysis
  • Dendritic Cells / pathology
  • Dermatofibrosarcoma / pathology*
  • Diagnosis, Differential
  • Humans
  • Male
  • Skin / pathology
  • Skin Neoplasms / pathology*

Substances

  • Biomarkers, Tumor