Alveolar capillary dysplasia with congenital misalignment of pulmonary vessels

Asian Cardiovasc Thorac Ann. 2005 Mar;13(1):82-4. doi: 10.1177/021849230501300121.


Alveolar capillary dysplasia with misalignment of pulmonary vessels is an uncommon congenital cause of persistent pulmonary hypertension of the newborn. It is universally fatal, and diagnosis is entirely dependent upon surgical lung biopsy. We present a case of alveolar capillary dysplasia with misalignment of pulmonary vessels occurring in a full-term neonate, emphasizing that early involvement of the thoracic surgeon for a histological diagnosis allows expensive and ineffective treatments to be avoided.

Publication types

  • Case Reports

MeSH terms

  • Capillaries / abnormalities*
  • Fatal Outcome
  • Female
  • Humans
  • Hypertension, Pulmonary / etiology
  • Infant, Newborn
  • Pulmonary Alveoli / blood supply*
  • Pulmonary Artery / abnormalities*
  • Pulmonary Veins / abnormalities*