Inferior sinus venosus defect associated with incomplete cor triatriatum dexter and patent foramen ovale

Eur J Echocardiogr. 2006 Jun;7(3):239-42. doi: 10.1016/j.euje.2005.04.006.

Abstract

Sinus venosus atrial septal defect (SVD) is a rare cardiac abnormality in adults. Particularly, the inferior type is difficult to depict by transthoracic echocardiography because of its infero-posterior location to the fossa ovalis. We describe the case of a 33-year-old woman whose chest X-ray taken during bronchopneumonia revealed a cardiomegaly. Further echocardiographic investigations showed an underlying inferior SVD, an incomplete cor triatriatum dexter and a large patent foramen ovale (PFO). The diagnosis was confirmed by cardiac magnetic resonance imaging (CMR) and during surgical repair.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Cor Triatriatum / diagnostic imaging*
  • Cor Triatriatum / surgery
  • Diagnosis, Differential
  • Female
  • Heart Septal Defects, Atrial / diagnostic imaging*
  • Heart Septal Defects, Atrial / surgery
  • Humans
  • Magnetic Resonance Imaging
  • Ultrasonography