Freeman-Sheldon syndrome: dental and orthodontic implications

J Clin Pediatr Dent. Spring 2005;29(3):267-71. doi: 10.17796/jcpd.29.3.8576133xh3576n76.


The manifestations of the Freeman-Sheldon syndrome (FSS) in four members of a South African family of Xhosa stock have been documented. Orofacial manifestations are a major syndromic component and warrant early, specialized orthodontic intervention. Our protocol for dental management is outlined and suggestions for holistic oro-dental care are provided.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Dental Care
  • Facies*
  • Female
  • Hand Deformities, Congenital / diagnostic imaging
  • Humans
  • Infant
  • Maxillofacial Abnormalities / diagnostic imaging
  • Maxillofacial Abnormalities / therapy*
  • Microstomia / therapy*
  • Patient Care Planning
  • Radiography
  • Syndrome