Primary pulmonary lymphoma: current status

Clin Lymphoma Myeloma. 2005 Nov;6(3):220-7. doi: 10.3816/CLM.2005.n.049.


Primary pulmonary lymphoma (PPL) is a rare disease with a favorable prognosis compared with lung cancer. Although a number of histologic variables of B- and T-cell lymphoma were reported as PPL, marginal zone lymphoma of the mucosa-associated lymphoid tissue type is by far the most frequent diagnosis. This review summarizes the present knowledge of histopathology, molecular biology, diagnosis, prognosis, and treatment of this heterogeneous entity.

Publication types

  • Review

MeSH terms

  • Diagnosis, Differential
  • Humans
  • Lung Neoplasms / pathology
  • Lung Neoplasms / physiopathology*
  • Lung Neoplasms / therapy*
  • Lymphoma, Non-Hodgkin / pathology
  • Lymphoma, Non-Hodgkin / physiopathology*
  • Lymphoma, Non-Hodgkin / therapy*
  • Prognosis