Background: The authors present an unusual complication of mandibular distraction in a child with the curious condition of multiple pterygium syndrome is presented.
Case report: The patient was a Caucasian male with severe pterygia in his neck. As a result of his limited mouth opening and restricted upper airway leading to obstruction, he underwent lengthening of his mandible by distraction, which significantly improved his breathing. During his follow-up, it was observed that an unusually elongated permanent molar was present in an abnormal position.
Conclusion: This case highlights the need to carefully plan the sites for osteotomy and the potential for damage to the developing permanent dentition in young children.