Pulmonary venous stenosis as an associated manifestation of left-sided obstructive lesions in an infant with partial atrioventricular canal defect

Pediatr Cardiol. 2005 Jul-Aug;26(4):449-51. doi: 10.1007/s00246-005-8640-8.


Patients with partial atrioventricular canal defect (PAVC) who present with congestive heart failure within the first year of life are usually found to have associated left-sided obstructive lesions. We present a case of a child with PAVC who subsequently developed progressive pulmonary venous stenosis as a manifestation of her disease.

Publication types

  • Case Reports

MeSH terms

  • Angiography
  • Cardiac Surgical Procedures / methods
  • Disease Progression
  • Echocardiography
  • Endocardial Cushion Defects / complications*
  • Endocardial Cushion Defects / diagnosis
  • Endocardial Cushion Defects / surgery
  • Fatal Outcome
  • Female
  • Heart Failure / diagnosis
  • Heart Failure / etiology*
  • Heart Failure / surgery
  • Humans
  • Infant, Newborn
  • Pulmonary Veno-Occlusive Disease / complications*
  • Pulmonary Veno-Occlusive Disease / diagnosis
  • Pulmonary Veno-Occlusive Disease / surgery
  • Vascular Surgical Procedures / methods