Lower eyelid entropion in Langer-Giedion syndrome

Ophthalmic Plast Reconstr Surg. 2006 Jan-Feb;22(1):59-60. doi: 10.1097/01.iop.0000194987.39325.49.


Langer-Giedion syndrome results from a genetic deletion on chromosome 8. Although redundant skin is part of Langer-Giedion syndrome, lower eyelid entropion and eyelid laxity have not been previously reported in the medical literature. We report a case of bilateral lower eyelid entropion in a patient with Langer-Giedion syndrome who successfully underwent entropion repair with anterior lamellar resection, lower eyelid retractor advancement, and lateral canthopexy. Although she has done well 6 months after surgery, we anticipate that laxity and eyelid instability will continue to develop with age, and additional reconstructive surgery may be required.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Blepharoplasty / methods*
  • Entropion / etiology*
  • Entropion / surgery
  • Female
  • Follow-Up Studies
  • Humans
  • Langer-Giedion Syndrome / complications*