Atrioventricular septal defect with intact septal structures presenting as left atrioventricular valvar insufficiency

Cardiol Young. 2006 Feb;16(1):92-4. doi: 10.1017/S1047951105002180.


We describe the findings in a six-year-old girl who presented with signs of left atrioventricular valvar insufficiency. The echocardiogram showed a common atrioventricular junction, intact atrial and ventricular septal structures. At surgery, the left-sided atrioventricular valve was found to be tri-foliate, and corrected by valvoplasty. To the best of our knowledge, this is the first case of atrioventricular septal defect with common atrioventricular junction and intact septal structures diagnosed during life.

Publication types

  • Case Reports

MeSH terms

  • Cardiac Surgical Procedures / methods
  • Child
  • Diagnosis, Differential
  • Echocardiography
  • Electrocardiography
  • Female
  • Heart Septal Defects / complications
  • Heart Septal Defects / diagnosis*
  • Heart Septal Defects / surgery
  • Heart Valve Diseases / complications
  • Heart Valve Diseases / diagnosis
  • Heart Valve Diseases / surgery
  • Heart Valves / abnormalities*
  • Heart Valves / surgery
  • Humans
  • Suture Techniques