Enlarged left vitelline vein remnant as a cause of cyanosis after the Fontan procedure: resolution with an Amplatzer vascular plug

Pediatr Cardiol. 2006 May-Jun;27(3):381-4. doi: 10.1007/s00246-005-1270-3.

Abstract

A 6-year-old girl with heterotaxy and a functional single ventricle had persistent cyanosis 4 years after a fenestrated Fontan procedure. Cardiac catheterization revealed a large venous fistula from a left-sided hepatic vein to the coronary sinus, resulting in desaturation. The anomalous vein was occluded with an Amplatzer vascular plug.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Collateral Circulation* / physiology
  • Coronary Angiography
  • Coronary Circulation* / physiology
  • Cyanosis / etiology*
  • Cyanosis / therapy*
  • Female
  • Fontan Procedure / adverse effects*
  • Hepatic Veins / diagnostic imaging
  • Humans
  • Prostheses and Implants*
  • Pulmonary Circulation
  • Vascular Fistula / complications
  • Vascular Fistula / etiology*
  • Vascular Fistula / therapy*
  • Veins / embryology