Segmental multicystic dysplasia and ureteropelvic junction obstruction in a nonduplicated kidney

J Pediatr Surg. 2006 Apr;41(4):e1-3. doi: 10.1016/j.jpedsurg.2006.01.056.


A 2-month-old child presented for evaluation of prenatal hydronephrosis. Imaging studies were consistent with a right duplex system with a dysplastic, nonfunctioning upper pole and lower pole ureteropelvic junction obstruction. We proceeded with removal of the upper pole and pyeloplasty and were surprised to find a single collecting system with a cystic, dysplastic upper pole segment and the absence of an upper pole pelvis or ureter. The rare diagnosis of a segmental multicystic dysplastic kidney with ipsilateral ureteropelvic junction obstruction was made. We present a review of the case and of previous literature on this topic.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Female
  • Humans
  • Infant
  • Kidney Pelvis*
  • Multicystic Dysplastic Kidney* / complications
  • Multicystic Dysplastic Kidney* / diagnosis
  • Multicystic Dysplastic Kidney* / surgery
  • Ureteral Obstruction* / complications
  • Ureteral Obstruction* / diagnosis
  • Ureteral Obstruction* / surgery