Pulmonary vein stenosis following repair of total anomalous pulmonary venous connection

Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu. 2006;51-5. doi: 10.1053/j.pcsu.2006.02.023.


Pulmonary vein stenosis may occur following the repair of total anomalous pulmonary venous connection and carries a poor prognosis. Conventional surgical therapies have been complicated by a high rate of re-stenosis. Sutureless pericardial marsupialization has been introduced as a technique to reduce the rate of re-stenosis. This report describes a retrospective review of a group of patients undergoing repair of acquired pulmonary vein stenosis. Presence of single-ventricle anatomy was found to be the primary preoperative risk factor for a poor outcome. The use of sutureless pericardial marsupialization was found to be associated with a significant improvement in disease-free survival.

MeSH terms

  • Anastomosis, Surgical / adverse effects
  • Cardiac Surgical Procedures / adverse effects*
  • Child, Preschool
  • Constriction, Pathologic
  • Female
  • Heart Atria / surgery
  • Heart Defects, Congenital / surgery*
  • Humans
  • Infant
  • Male
  • Pulmonary Veins / abnormalities*
  • Pulmonary Veins / surgery*
  • Pulmonary Veno-Occlusive Disease / etiology
  • Pulmonary Veno-Occlusive Disease / surgery*
  • Survival Analysis
  • Treatment Outcome