Multiple developmental dental anomalies and hypermobility type Ehlers-Danlos syndrome

J Clin Pediatr Dent. 2006 Summer;30(4):337-41. doi: 10.17796/jcpd.30.4.72426m58695tg2h0.


Concurrent existence of multiple developmental dental anomalies: hypodontia of permanent mandibular incisors, dentin dysplasia, transmigration, root dilaceration, ectopic eruption and delayed eruption combined with systemic abnormalities including joint hyperlaxity and skin hyperextensibility aided in diagnosis of a sporadic case of hypermobility type of Ehlers-Danlos syndrome in a Jordanian Arab male. In dental practice the presence of multiple developmental dental anomalies expressing simultaneous defects in different stages of tooth development should raise suspicion of possible of manifestation of an underlying systemic abnormality.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Anodontia / diagnostic imaging
  • Anodontia / etiology*
  • Ehlers-Danlos Syndrome / complications*
  • Humans
  • Joint Instability / etiology*
  • Male
  • Radiography
  • Tooth, Unerupted / diagnostic imaging
  • Tooth, Unerupted / etiology*