Freeman-Sheldon syndrome: a case report

Int J Paediatr Dent. 2006 Nov;16(6):440-3. doi: 10.1111/j.1365-263X.2006.00742.x.


Background: Freeman-Sheldon Syndrome is a rare craniofacial syndrome that has not been described in the dental literature to date. The main feature of relevance is severe microstomia, which limits access for routine dental care.

Case report: Dental treatment was carried out successfully under local anaesthetic for a young child with Freeman-Sheldon syndrome. A novel coloured compomer material was helpful in the management of the case.

Conclusion: The importance of early referral of children with rare craniofacial anomalies to Specialist Paediatric Dental services is highlighted.

Publication types

  • Case Reports

MeSH terms

  • Child, Preschool
  • Compomers
  • Craniofacial Abnormalities / pathology*
  • Dental Caries / therapy*
  • Dental Restoration, Permanent / methods
  • Female
  • Follow-Up Studies
  • Humans
  • Microstomia / pathology*
  • Molar
  • Pit and Fissure Sealants / therapeutic use
  • Tooth, Deciduous / pathology


  • Compomers
  • Pit and Fissure Sealants