The role of spiral multidetector dynamic CT in the study of Williams-Campbell syndrome

Acta Radiol. 2006 Oct;47(8):798-800. doi: 10.1080/02841850600849084.


Williams-Campbell syndrome is a cystic bronchiectatic disease secondary to deficiency or defect of cartilaginous plates in the wall of the airways. In the literature, two main forms are suggested: congenital and acquired (post-infectious). The most frequent symptoms are represented by recurrent pulmonary infections from childhood. Multislice spiral dynamic CT has a major role in the study of cystic pulmonary disease and in differentiating Williams-Campbell syndrome from the other causes of cystic bronchiectasis, in which even lung function tests can give deceptive results.

Publication types

  • Case Reports

MeSH terms

  • Bronchi / abnormalities*
  • Bronchiectasis / congenital
  • Bronchiectasis / diagnostic imaging*
  • Bronchiectasis / etiology
  • Cartilage / abnormalities*
  • Humans
  • Syndrome
  • Tomography, Spiral Computed*