Neonatal screening for congenital hypothyroidism in the Netherlands: cognitive and motor outcome at 10 years of age

J Clin Endocrinol Metab. 2007 Mar;92(3):919-24. doi: 10.1210/jc.2006-1538. Epub 2006 Dec 12.

Abstract

Context: Patients with thyroidal congenital hypothyroidism (CH-T) born in The Netherlands in 1981-1982 showed persistent intellectual and motor deficits during childhood and adulthood, despite initiation of T(4) supplementation at a median age of 28 d after birth.

Objective: The present study examined whether advancement of treatment initiation to 20 d had resulted in improved cognitive and motor outcome.

Design/setting/patients: In 82 Dutch CH-T patients, born in 1992 to 1993 and treated at a median age of 20 d (mean, 22 d; range, 2-73 d), cognitive and motor outcome was assessed (mean age, 10.5 yr; range, 9.6-11.4 yr). Severity of CH-T was classified according to pretreatment free T(4) concentration.

Main outcome measure: Cognitive and motor outcome of the 1992-1993 cohort in comparison to the 1981 to 1982 cohort was the main outcome measure.

Results: Patients with severe CH-T had lower full-scale (93.7), verbal (94.9), and performance (93.9) IQ scores than the normative population (P < 0.05), whereas IQ scores of patients with moderate and mild CH-T were comparable to those of the normative population. In all three severity subgroups, significant motor problems were observed, most pronounced in the severe CH-T group. No correlations were found between starting day of treatment and IQ or motor outcome.

Conclusions: Essentially, findings from the 1992-1993 cohort were similar to those of the 1981-1982 cohort. Apparently, advancing initiation of T(4) supplementation from 28 to 20 d after birth did not result in improved cognitive or motor outcome in CH-T patients.

Publication types

  • Comparative Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Child
  • Cohort Studies
  • Congenital Hypothyroidism / complications*
  • Congenital Hypothyroidism / diagnosis*
  • Congenital Hypothyroidism / drug therapy
  • Female
  • Follow-Up Studies
  • Humans
  • Infant, Newborn
  • Intelligence*
  • Male
  • Motor Skills*
  • Neonatal Screening*
  • Netherlands
  • Thyroxine / therapeutic use
  • Time Factors

Substances

  • Thyroxine