Abnormal length of cilia--a cause of primary ciliary dyskinesia--a case report

Eur J Pediatr. 1992 Jan;151(1):73-5. doi: 10.1007/BF02073899.


A 7-year-old Turkish boy had suffered from chronic coughing from early childhood. Severe bronchiectasis in the right lung was confirmed by bronchography. Ciliary beat frequency determined in a bronchial mucosal biopsy was markedly decreased (5.7 Hz). Electron microscopy revealed cilia with a length of 15 microns. No structural abnormality was found. A possible link between the abnormally long, slow beating cilia and the clinical symptoms is discussed.

Publication types

  • Case Reports

MeSH terms

  • Bronchi
  • Bronchiectasis / complications
  • Bronchiectasis / diagnostic imaging*
  • Child
  • Chronic Disease
  • Ciliary Motility Disorders / complications*
  • Ciliary Motility Disorders / pathology
  • Ciliary Motility Disorders / physiopathology
  • Cough / etiology*
  • Humans
  • Male
  • Mucociliary Clearance
  • Mucous Membrane / ultrastructure
  • Radiography