A spontaneously ruptured primitive neuroectodermal tumor/extraosseous Ewing's sarcoma of the kidney with renal vein tumor thrombus

Int Urol Nephrol. 2007;39(2):393-5. doi: 10.1007/s11255-006-9073-x. Epub 2007 Feb 20.


Primitive neuroectodermal tumor/extraosseous Ewing's sarcoma (PNET/EES) is a childhood disease rarely seen in adults. It is a soft tissue tumor, which is often observed in the paraspinal region and lower extremity. We report the case of a 32-year-old man who presented with sudden abdominal pain on the right upper quadrant that was radiated to the right flank. During the operation, a spontaneously ruptured right kidney mass was found. The histopathologic and immunohistochemical characteristics of the excised mass were consistent with PNET/EES. This is the first known reported case of spontaneously ruptured PNET/EES of the kidney with renal vein tumor thrombus. The clinical details and the management of this case are described.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Humans
  • Kidney Neoplasms / complications*
  • Male
  • Neoplastic Cells, Circulating*
  • Neuroectodermal Tumors, Primitive / complications*
  • Renal Veins*
  • Rupture, Spontaneous
  • Sarcoma, Ewing / complications*