Hughes-Stovin syndrome: is it incomplete Behçet's? Report of two cases and review of the literature

Clin Rheumatol. 2007 Nov;26(11):1993-6. doi: 10.1007/s10067-007-0609-y. Epub 2007 Apr 25.

Abstract

In this report, we described two male patients with Hughes-Stovin syndrome. The first patient was a 26-year-old male who initially presented with deep vein thrombosis (DVT) in the right lower limb followed shortly by hemoptysis. Pulmonary CT angiography revealed bilateral pulmonary artery aneurysms secondary to underlying pulmonary vasculitis. While the second case was a 16-year-old male patient who initially presented with generalized fits due to sagittal sinus thrombosis and later followed by DVT in the left lower limb. Pulmonary CT angiography showed small pulmonary artery aneurysms with thrombosis of peripheral pulmonary artery branches. Both patients were treated successfully with steroids and immunosuppressive therapy and showed clinical improvement.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Adult
  • Aneurysm / diagnosis*
  • Aneurysm / pathology
  • Angiography / methods
  • Behcet Syndrome / diagnosis*
  • Behcet Syndrome / pathology
  • Diagnosis, Differential
  • Humans
  • Immunosuppressive Agents / therapeutic use
  • Magnetic Resonance Imaging
  • Male
  • Pulmonary Artery / pathology*
  • Syndrome
  • Tomography, X-Ray Computed
  • Vasculitis / diagnosis*
  • Vasculitis / pathology
  • Venous Thrombosis / diagnosis*
  • Venous Thrombosis / pathology

Substances

  • Immunosuppressive Agents