Laparoscopic findings and pelvic anatomy in Mayer-Rokitansky-Küster-Hauser syndrome

Obstet Gynecol. 2007 May;109(5):1111-5. doi: 10.1097/01.AOG.0000260872.28368.46.


Objective: To describe analytically the anatomic variety and laparoscopic findings observed in patients with Rokitansky syndrome throughout an 11-year span.

Methods: We analyzed the laparoscopic and chart records of 106 consecutive patients who underwent surgery for the creation of a neovagina, according to the modified laparoscopic Vecchietti procedure.

Results: A hypoplastic vagina was observed in 61 women. Müllerian remnants, laterally displaced in the pelvis, were identified in 92 cases; 42 (25.9%, 95% confidence interval [CI] 19.2-33.3) of 162 müllerian remnants were cavitated and contained endometrial mucosa. Ovaries were extrapelvic in 17 (16.0%, 95% CI 9.6-24.4) cases. Anomalies of the urinary tract were identified in 32 (30.2%, 95% CI 21.7-39.9) patients; unilateral renal agenesis was the most frequent finding (18 cases; 18%, 95%CI 10.4-25.5).

Conclusion: Rokitansky syndrome has a wide variability of anatomic presentations, and, as the do other congenital anomalies of the female genital tract, it represents a continuum of embryonic malformations, which occur at different stages of development.

MeSH terms

  • Adolescent
  • Adult
  • Female
  • Humans
  • Laparoscopy
  • Syndrome
  • Uterus / abnormalities*
  • Vagina / abnormalities*