Abstract
We describe a woman in whom hypogammaglobulinemia and severe granulomatous cutaneous lesions had developed during childhood; subsequently, Hodgkin's disease and necrobiotic xanthogranuloma were diagnosed. This case illustrates an apparent association with disease activity and raises the question of a direct relationship of necrobiotic xanthogranuloma with lymphoproliferative disease.
MeSH terms
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Adolescent
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Agammaglobulinemia / complications*
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Agammaglobulinemia / diagnosis
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Agammaglobulinemia / therapy
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Biopsy
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Bone Marrow Examination
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Female
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Hodgkin Disease / complications*
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Hodgkin Disease / diagnosis
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Hodgkin Disease / therapy
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Humans
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Neoplasm Staging
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Paraproteinemias / complications*
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Paraproteinemias / diagnosis
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Paraproteinemias / therapy
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Recurrence
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Tomography, X-Ray Computed
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Xanthogranuloma, Juvenile / complications*
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Xanthogranuloma, Juvenile / diagnosis
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Xanthogranuloma, Juvenile / therapy