Osteomas are benign osteogenic lesions with very slow growth, which may arise from proliferation of either cancellous or compact bone. In the jaw, these are uncommon lesions. Excluding the maxillary sinus, there are only eight cases of maxillary osteoma reported in the English-language literature. This paper reports an additional case of maxillary osteoma in a 40-year-old man. We discuss the clinical data from the previously described cases and the main differential diagnoses.