Target proteins of C/EBPalphap30 in AML: C/EBPalphap30 enhances sumoylation of C/EBPalphap42 via up-regulation of Ubc9

Blood. 2007 Nov 1;110(9):3301-9. doi: 10.1182/blood-2007-01-071035. Epub 2007 Aug 1.

Abstract

CCAAT/enhancer-binding protein alpha (C/EBPalpha) is a critical regulator for early myeloid differentiation. Mutations in C/EBPalpha occur in 10% of patients with acute myeloid leukemia (AML), leading to the expression of a 30-kDa dominant-negative isoform (C/EBPalphap30). In the present study, using a global proteomics approach to identify the target proteins of C/EBPalphap30, we show that Ubc9, an E2-conjugating enzyme essential for sumoylation, is increased in its expression when C/EBPalphap30 is induced. We confirmed the increased expression of Ubc9 in patients with AML with C/EBPalphap30 mutations compared with other subtypes. We further confirmed that the increase of Ubc9 expression was mediated through increased transcription. Furthermore, we show that Ubc9-mediated enhanced sumoylation of C/EBPalphap42 decreases the transactivation capacity on a minimal C/EBPalpha promoter. Importantly, overexpression of C/EBPalphap30 in granulocyte colony-stimulating factor (G-CSF)-stimulated human CD34(+) cells leads to a differentiation block, which was overcome by the siRNA-mediated silencing of Ubc9. In summary, our data indicate that Ubc9 is an important C/EBPalphap30 target through which C/EBPalphap30 enhances the sumoylation of C/EBPalphap42 to inhibit granulocytic differentiation.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • CCAAT-Enhancer-Binding Proteins / genetics
  • CCAAT-Enhancer-Binding Proteins / metabolism*
  • CCAAT-Enhancer-Binding Proteins / physiology*
  • Cell Differentiation / genetics
  • Gene Expression Regulation, Leukemic
  • Gene Silencing
  • Genes, Dominant / physiology
  • Granulocytes / cytology
  • Humans
  • K562 Cells
  • Leukemia, Myeloid, Acute / genetics*
  • Lysine / metabolism
  • Models, Biological
  • Mutant Proteins / genetics
  • Mutant Proteins / metabolism
  • Mutant Proteins / physiology*
  • Protein Isoforms / genetics
  • Protein Isoforms / metabolism
  • Protein Processing, Post-Translational / genetics*
  • Receptors, Estrogen / genetics
  • SUMO-1 Protein / metabolism*
  • Transcriptional Activation
  • Ubiquitin-Conjugating Enzyme UBC9
  • Ubiquitin-Conjugating Enzymes / genetics*
  • Up-Regulation*

Substances

  • CCAAT-Enhancer-Binding Proteins
  • CEBPA protein, human
  • Mutant Proteins
  • Protein Isoforms
  • Receptors, Estrogen
  • SUMO-1 Protein
  • Ubiquitin-Conjugating Enzymes
  • Ubiquitin-Conjugating Enzyme UBC9
  • Lysine