Severe nephropathy in three adolescents with cystic fibrosis

Arch Dis Child. 1991 Dec;66(12):1444-7. doi: 10.1136/adc.66.12.1444.


Renal involvement has rarely been reported in patients with cystic fibrosis. We describe severe nephropathy with a rapidly fatal outcome in three adolescents with cystic fibrosis, and evaluate the important repercussions that the nephrotic syndrome had on the precarious clinical situation of these patients.

MeSH terms

  • Adolescent
  • Cystic Fibrosis / complications*
  • Female
  • Humans
  • Kidney Failure, Chronic / etiology
  • Male
  • Nephrotic Syndrome / etiology*
  • Prognosis
  • Proteinuria / etiology
  • Time Factors