Isolated junctional tachycardia in a patient with pheochromocytoma: an unusual presentation of an uncommon disease

Pediatr Cardiol. 2008 Sep;29(5):986-8. doi: 10.1007/s00246-007-9134-7. Epub 2007 Nov 8.


Pheochromocytoma is a rare disease, which often presents a diagnostic challenge due to a variable symptom presentation complex. We report the case of a child who presented with isolated symptoms of palpitations and was found to have junctional tachycardia with subsequent development of cardiomyopathy. Further evaluation revealed that she had an extra-adrenal pheochromocytoma, which was the cause of her arrhythmia and subsequent symptomatology.

Publication types

  • Case Reports

MeSH terms

  • Cardiomyopathies / etiology
  • Child
  • Electrocardiography
  • Female
  • Humans
  • Paraganglioma, Extra-Adrenal / complications*
  • Paraganglioma, Extra-Adrenal / surgery
  • Retroperitoneal Neoplasms / complications*
  • Retroperitoneal Neoplasms / surgery
  • Tachycardia, Ectopic Junctional / diagnosis
  • Tachycardia, Ectopic Junctional / etiology*