Basal Encephalocele Associated With Morning Glory Syndrome: Case Report

Arq Neuropsiquiatr. 2007 Dec;65(4A):988-91. doi: 10.1590/s0004-282x2007000600013.


The basal encephaloceles refer to rare entities and they correspond to herniation of brain tissue through defects of skull along the cribiform plate or the sphenoid bone. A rare morning glory syndrome, with characteristic retinal defect has been reported in association with basal encephaloceles. Hypophysis hormonal deficiencies may occur. We accounted for a pituitary dwarfism with delayed diagnosed transsphenoidal encephalocele associated with morning glory syndrome, showing the alterations found in retinography, computed tomography and magnetic resonance imaging.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Dwarfism, Pituitary / complications*
  • Dwarfism, Pituitary / diagnosis
  • Encephalocele / complications*
  • Encephalocele / diagnosis
  • Fundus Oculi
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Optic Disk / abnormalities*
  • Optic Disk / pathology
  • Syndrome
  • Tomography, X-Ray Computed