Objective: To reestablish uterovaginal continuity using a total laparoscopic procedure in Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome with a functioning right horn.
Design: Case report.
Setting: University hospital of Hotel Dieu de Lyon.
Patient(s): A 13-year-old woman with cyclic abdominal pain. We diagnosed MRKH syndrome with cyclic pain due to a hematometra in a functioning right horn associated to a right hematosalpinx and a nonfunctioning left horn.
Intervention(s): Reestablishing uterovaginal continuity with excision of the left rudimentary horn via a total laparoscopic procedure.
Main outcome measure(s): Restoring regular menstruation.
Result(s): After total laparoscopic uterovaginal anastomosis and excision of the left nonfunctioning horn, the patient's menstruation resumed 3 months later, and regular, unimpeded menstrual flow was still present at the 2-year-follow-up evaluation.
Conclusion(s): Total laparoscopic reestablishment of uterovaginal continuity in MRKH syndrome with a functioning horn is a valuable alternative to the currently recommended treatment (laparotomy and radical excision of the rudimentary uterus).