Cardiac rhabdomyoma

Cardiovasc Pathol. 2009 Sep-Oct;18(5):313-4. doi: 10.1016/j.carpath.2008.02.002. Epub 2008 Apr 15.


Primary tumors of the heart are exceedingly rare with a prevalence rate of around 0.01% in autopsy studies. A majority of primary cardiac tumors are benign. Rhabdomyomas are the most common of benign pediatric cardiac tumors. A newborn female infant presented with perioral cyanosis and respiratory distress. She deteriorated progressively. The infant expired, and at autopsy, dissection of the heart revealed a large tumor mass in the interventricular septum. Histologically, the mass showed the classic "spider cells," and a diagnosis of cardiac rhabdomyoma of childhood was established.

Publication types

  • Case Reports

MeSH terms

  • Cyanosis / etiology
  • Fatal Outcome
  • Female
  • Heart Neoplasms / complications
  • Heart Neoplasms / pathology*
  • Humans
  • Infant, Newborn
  • Respiratory Distress Syndrome, Newborn / etiology
  • Rhabdomyoma / complications
  • Rhabdomyoma / pathology*