Motor variant of chronic inflammatory demyelinating polyneuropathy in a child

Pediatr Neurol. 2008 Jun;38(6):426-9. doi: 10.1016/j.pediatrneurol.2008.02.008.

Abstract

Only 2 cases of pure motor chronic demyelinating inflammatory polyneuropathy in the pediatric age group have been reported in the literature. We report on a motor variant of chronic demyelinating inflammatory polyneuropathy with anti-ganglioside antibodies, diagnosed in a 5-year-old girl who presented with progressive motor weakness over a period of 12 months with no sensory involvement. She initially responded partially to intravenous immunoglobulin therapy (1 gm/kg/month for 6 months), and then demonstrated sustained but incomplete improvement on chronic prednisone therapy (1-2 mg/kg/day), on which she has continued since 1 year and 4 months after her initial presentation 3 years ago.

Publication types

  • Case Reports

MeSH terms

  • Anti-Inflammatory Agents / therapeutic use
  • Biopsy
  • Child, Preschool
  • Electrodiagnosis
  • Electroencephalography
  • Electromyography
  • Female
  • Humans
  • Magnetic Resonance Imaging
  • Motor Neuron Disease / cerebrospinal fluid
  • Motor Neuron Disease / pathology
  • Motor Neuron Disease / physiopathology*
  • Muscle Weakness / etiology
  • Neural Conduction
  • Polyneuropathies / cerebrospinal fluid
  • Polyneuropathies / pathology
  • Polyneuropathies / physiopathology*
  • Prednisone / therapeutic use

Substances

  • Anti-Inflammatory Agents
  • Prednisone