Pseudoxanthoma elasticum (PXE) is a rare form of congenital dystrophy of the elastic tissue, which is characterized by cutaneous, ocular and vascular impact. There are four clinical forms which correspond to 4 different genetic types (I or II, dominant or recessive). The vascular damage caused by the illness general limits the obstetric prognosis. Under our observation, the pregnancy of a woman 34 years of age suffering from type II PXE proceeded without problem.