Retroperitoneal fibrosis: a review of clinical features and imaging findings

AJR Am J Roentgenol. 2008 Aug;191(2):423-31. doi: 10.2214/AJR.07.3629.


Objective: Retroperitoneal fibrosis is a rare collagen vascular disorder of unclear cause. Both benign and malignant associations have been described, rendering differentiation of these entities of paramount importance because sinister pathology alters the diagnosis. Thus, a high level of diligence is required in the investigation of this condition, particularly in patients with concomitant systemic conditions.

Conclusion: Familiarity with the realm of imaging manifestations of retroperitoneal fibrosis is vital to ensure correct diagnosis and optimal treatment.

Publication types

  • Review

MeSH terms

  • Contrast Media
  • Diagnosis, Differential
  • Diagnostic Imaging*
  • Humans
  • Incidence
  • Retroperitoneal Fibrosis / diagnosis*
  • Retroperitoneal Fibrosis / epidemiology
  • Retroperitoneal Fibrosis / pathology


  • Contrast Media