Cardiac Papillary Fibroelastoma: case report and review of the literature

Int J Cardiol. 2010 Feb 18;139(1):102-4. doi: 10.1016/j.ijcard.2008.06.092. Epub 2008 Aug 20.


Primary cardiac tumors are very rare. Cardiac Papillary Fibroelastoma (CPF) is the third most common primary tumor of the heart and most commonly affects cardiac valves. Those tumors appear like a "sea anemone" with multiple papillary fronds attached to the endocardium by a short stalk. It generally occurs as a single structure and is typically found on the atrial aspect of atrioventricular valves or either side of the semilunar valves. We report a case of aortic valve papillary fibroelastoma which was found on autopsy in a patient with normal coronary artery with evidence of myocardial and cerebral ischemic damage and sudden death.

Publication types

  • Case Reports
  • Letter
  • Review

MeSH terms

  • Aortic Valve / pathology*
  • Fatal Outcome
  • Fibroma / pathology*
  • Heart Neoplasms / pathology*
  • Humans
  • Male
  • Middle Aged
  • Papillary Muscles / pathology*