The higher level of organization of the oxidative phosphorylation system: mitochondrial supercomplexes

J Bioenerg Biomembr. 2008 Oct;40(5):419-24. doi: 10.1007/s10863-008-9167-5. Epub 2008 Oct 7.

Abstract

The organization of the oxidative phosphorylation (OXPHOS) system within the inner mitochondrial membrane appears to be far more complicated than previously thought. In particular, the individual protein complexes of the OXPHOS system (complexes I to V) were found to specifically interact forming defined supramolecular structures. Blue-native polyacrylamide gel electrophoresis and single particle electron microscopy proved to be especially valuable in studying the so-called "respiratory supercomplexes". Based on these procedures, increasing evidence was presented supporting a "solid state" organization of the OXPHOS system. Here, we summarize results on the formation, organisation and function of the various types of mitochondrial OXPHOS supercomplexes.

Publication types

  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Animals
  • Electron Transport Chain Complex Proteins / chemistry*
  • Electron Transport Chain Complex Proteins / metabolism*
  • Electron Transport Chain Complex Proteins / ultrastructure
  • Electrophoresis, Polyacrylamide Gel
  • Microscopy, Electron
  • Mitochondria / enzymology*
  • Mitochondrial Proton-Translocating ATPases / chemistry
  • Mitochondrial Proton-Translocating ATPases / metabolism
  • Mitochondrial Proton-Translocating ATPases / ultrastructure
  • Models, Biological
  • Models, Molecular
  • Oxidative Phosphorylation*
  • Protein Structure, Quaternary

Substances

  • Electron Transport Chain Complex Proteins
  • Mitochondrial Proton-Translocating ATPases