Mayer-Rokitansky-Kuster-Hauser syndrome associated with endodermal sinus tumor of the ovary

Fertil Steril. 1991 Sep;56(3):577-8. doi: 10.1016/s0015-0282(16)54562-2.


Both EST and Mayer-Rokitansky-Kuster-Hauser syndrome are uncommon disorders. This report illustrates a case of these two rare conditions occurring in the same patient. Patients with Mayer-Rokitansky-Kuster-Hauser syndrome, although not appearing to be at increased risk for germ cell tumors, unlike testicular feminization patients, are not immune to ovarian cancer. Therefore, individuals with Mayer-Rokitansky-Kuster-Hauser syndrome should still be followed gynecologically because they are at least at the normal risk of developing ovarian as well as other gynecological neoplasms.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Female
  • Humans
  • Mesonephroma / complications*
  • Mesonephroma / pathology
  • Ovarian Neoplasms / complications*
  • Ovarian Neoplasms / pathology
  • Syndrome
  • Uterus / abnormalities*
  • Vagina / abnormalities*