Phenotypic characterization of retinoblastoma for the presence of putative cancer stem-like cell markers by flow cytometry

Invest Ophthalmol Vis Sci. 2009 Apr;50(4):1506-14. doi: 10.1167/iovs.08-2356. Epub 2008 Nov 21.

Abstract

Purpose: Retinoblastoma (Rb) is an intraocular tumor that grows rapidly and poses a threat to sight and life. Similar to other tumors, there is increasing speculation that the Rb tumor also contains cancer stem-like cells that could influence the prognosis and response to therapy. This study was undertaken in an attempt to identify putative stem-like cells by characterizing different subpopulations of cells in retinoblastoma.

Methods: Freshly isolated tumor cells obtained from unfixed eye specimens (n=7) were analyzed for the presence of CD44, ABCG2, CXCR4, CD133, and CD90 using flow cytometry. RT-PCR was performed to analyze the expression of human Syntaxin1A, PROX1, CD133, and NSE in the sorted subpopulation of tumor cells.

Results: Two different subpopulations of cells were observed in seven samples. The small cells, assigned FSC(lo)/SSC(lo) (forward scatter low/side scatter low, ranging from 1.7% to 17.7%) were characterized as positive for CD44 and negative for CD133, CXCR4, and CD90. The large cells were designated as FSC(hi)/SSC(lo) (ranging from 2.7% to 35.1%) and characterized as positive for all markers. RT-PCR analysis revealed that sorted cells of FSC(lo)/SSC(lo) subpopulation expressed the retinal progenitor cell markers PROX1 and Syntaxin1A.

Conclusions: Retinoblastoma, on flow cytometric analysis, revealed two distinct subpopulations with variable expression of stem cell and retinal progenitor markers. In these populations, the FSC(lo)/SSC(lo) subpopulation appeared to be more primitive, since they expressed stem cell (CD44) and retinal progenitor markers (PROX1 and Syntaxin 1A) combined with a relatively lower percentage of differentiated markers. Moreover, the FSC(hi)/SSC(lo) subpopulation showed a higher percentage of differentiated markers (CD90 and CD133).

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • ATP Binding Cassette Transporter, Subfamily G, Member 2
  • ATP-Binding Cassette Transporters / analysis
  • Antigens, CD / analysis
  • Biomarkers, Tumor / analysis*
  • Carrier Proteins / analysis
  • Child
  • Child, Preschool
  • Female
  • Flow Cytometry / methods
  • Gene Expression Regulation, Neoplastic
  • Homeodomain Proteins / analysis
  • Humans
  • Infant
  • Male
  • Neoplasm Proteins / analysis*
  • Neoplastic Stem Cells / chemistry
  • Neoplastic Stem Cells / pathology*
  • Phenotype
  • Precancerous Conditions / pathology*
  • Receptors, CXCR4 / analysis
  • Retinal Neoplasms / chemistry
  • Retinal Neoplasms / pathology*
  • Retinoblastoma / chemistry
  • Retinoblastoma / pathology*
  • Reverse Transcriptase Polymerase Chain Reaction
  • Syntaxin 1 / analysis
  • Tumor Stem Cell Assay
  • Tumor Suppressor Proteins / analysis

Substances

  • ABCG2 protein, human
  • ATP Binding Cassette Transporter, Subfamily G, Member 2
  • ATP-Binding Cassette Transporters
  • Antigens, CD
  • Biomarkers, Tumor
  • CXCR4 protein, human
  • Carrier Proteins
  • Homeodomain Proteins
  • NSMCE1 protein, human
  • Neoplasm Proteins
  • Receptors, CXCR4
  • Syntaxin 1
  • Tumor Suppressor Proteins
  • prospero-related homeobox 1 protein