We report a case of hemimyelomeningocele. This is a rare spinal dysraphism, consisting of the association of a split cord malformation with myelomeningocele. MRI demonstrates division of the spinal cord into two hemicords which are separated by a bony spur. The left hemicord forms a myelomeningocele, thus resulting in a hemimyelomeningocele. Accurate and early diagnosis of spinal dysraphisms is essential for optimal, individualised neurosurgical treatment.