Surgery for endolymphatic sac tumor: whether and when to keep hearing?

Acta Otolaryngol. 2008 Sep;128(9):976-83. doi: 10.1080/00016480701808996.


Conclusion: Endolymphatic sac tumors (ELSTs) are locally invasive, osteolytic, and hypervascular tumors. If the labyrinth has not been invaded, the hearing should be preserved in operation.

Objective: To summarize three cases of ELST and discuss whether to keep hearing in the surgical treatment of ELST.

Subjects and methods: Complete otorhinolaryngological examinations with audiologic, vestibular, and neurologic evaluations were performed. CT and MRI scans were carried out before operation and in the course of follow-up. The patients underwent radical removal of the tumor through a transmastoid approach and accepted postoperative radiotherapy. In two of them, the structure of the labyrinth and facial nerve were preserved in operation.

Results: Histopathologic examinations agreed with features of an ELST. Patients suffered transitory vertigo shortly after operation, and so far, they are alive and well without further cranial nerve involvement. Case 3 patient has good hearing and facial nerve function now. No residual or recurrent tumor was detected on the postoperative MRI images.

Publication types

  • Case Reports

MeSH terms

  • Adenocarcinoma / diagnostic imaging
  • Adenocarcinoma / pathology*
  • Adenocarcinoma / surgery*
  • Adolescent
  • Adult
  • Ear Neoplasms / diagnostic imaging
  • Ear Neoplasms / pathology*
  • Ear Neoplasms / surgery*
  • Endolymphatic Sac*
  • Female
  • Hearing Loss / diagnosis
  • Hearing Loss / etiology
  • Hearing Loss / prevention & control*
  • Humans
  • Male
  • Radiography