Malignant triton tumor of the brachial plexus invading the left thoracic inlet: a rare differential diagnosis of pancoast tumor

J Thorac Oncol. 2009 Jan;4(1):135-7. doi: 10.1097/JTO.0b013e31819151ab.

Abstract

Malignant triton tumor is a divergent malignant peripheral nerve sheath tumor with rhabdomyoblastic differentiation. We report a case of malignant triton tumor arising in the brachial plexus of a 28-year-old women with neurofibromatosis type 1. Fluorodeoxyglucose-positron emission tomography-computed tomography before excision demonstrated a tumor with a maximum standard uptake value of 21 at 4 hours postinjection. The patient underwent complete excision of the tumor through median sternotomy and left supraclavicular approach. Adjuvant radiotherapy and chemotherapy were planned but the patient died of metastatic disease within 3 months of surgical resection.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Brachial Plexus / pathology*
  • Diagnosis, Differential
  • Fatal Outcome
  • Female
  • Fluorodeoxyglucose F18
  • Humans
  • Magnetic Resonance Imaging
  • Neoplasm Invasiveness
  • Neurilemmoma / diagnosis*
  • Neurilemmoma / surgery
  • Neurofibromatosis 1 / complications
  • Pancoast Syndrome / diagnosis*
  • Peripheral Nervous System Neoplasms / diagnosis*
  • Peripheral Nervous System Neoplasms / surgery
  • Positron-Emission Tomography
  • Radiopharmaceuticals
  • Thoracic Neoplasms / diagnosis*
  • Tomography, X-Ray Computed

Substances

  • Radiopharmaceuticals
  • Fluorodeoxyglucose F18