[Vasculitis multiple mononeuropathies]

Rev Prat. 2008 Nov 15;58(17):1896-9.
[Article in French]

Abstract

The impairment of the peripheral nervous system is frequent in primary or secondary vasculitis. The diagnosis of painful multiple mononeuropathy requires neuromuscular biopsy. Distal sensorimotor polyneuropathies are misleading. Therefore clinical and electrophysiological asymmetry is helpful. Steroids and cytotoxic agents have been the mainstay of therapy for most vasculitic neuropathies but therapeutic strategies may vary for ANCA-associated vasculitis.

Publication types

  • English Abstract

MeSH terms

  • Biopsy
  • Churg-Strauss Syndrome / complications
  • Diagnosis, Differential
  • Electromyography
  • Granulomatosis with Polyangiitis / complications
  • Humans
  • Immunosuppressive Agents / therapeutic use
  • Mononeuropathies / diagnosis
  • Mononeuropathies / drug therapy
  • Mononeuropathies / etiology*
  • Neuromuscular Junction / pathology
  • Polyarteritis Nodosa / complications
  • Polyneuropathies / diagnosis
  • Steroids / therapeutic use
  • Vasculitis / complications*

Substances

  • Immunosuppressive Agents
  • Steroids