Paraneoplastic fasciitis-panniculitis syndrome: a neurological point of view

Nat Clin Pract Neurol. 2009 Feb;5(2):113-7. doi: 10.1038/ncpneuro0999.

Abstract

Background: A 54-year-old woman who had undergone gastrectomy to treat gastric adenocarcinoma 5 years previously and had since been in remission presented to a neuromuscular clinic complaining of stiffening and painful spasms of the legs and abdomen. Repeat pan-CT scans and gastric biopsy confirmed the recurrence of poorly differentiated signet ring gastric adenocarcinoma. Her symptoms improved remarkably on initiation of chemotherapy and worsened on discontinuation of chemotherapy.

Investigations: Neurological examination, MRI of the abdomen and lower extremities, whole-body fluorodeoxyglucose PET, pan-CT scan, electromyography, muscle biopsy, upper gastrointestinal tract radiography, esophagogastroduodenoscopy, and immunophenotyping (paraneoplastic, rheumatological and autoimmune diseases panels).

Diagnosis: Paraneoplastic fasciitis-panniculitis syndrome associated with the recurrence of poorly differentiated signet ring gastric adenocarcinoma.

Management: Chemotherapy of recurrent gastric adenocarcinoma and symptomatic management of painful spasms.

Publication types

  • Case Reports

MeSH terms

  • Female
  • Gastrectomy / methods
  • Humans
  • Magnetic Resonance Imaging / methods
  • Middle Aged
  • Neoplasm Recurrence, Local*
  • Panniculitis* / complications
  • Panniculitis* / diagnosis
  • Panniculitis* / therapy
  • Paraneoplastic Syndromes* / complications
  • Paraneoplastic Syndromes* / diagnosis
  • Paraneoplastic Syndromes* / therapy
  • Positron-Emission Tomography
  • Stomach Neoplasms / surgery
  • Tomography, X-Ray Computed