Pregnancy outcome in patients with homozygous sickle cell disease in a university hospital, Eastern Saudi Arabia

Arch Gynecol Obstet. 2009 Nov;280(5):793-7. doi: 10.1007/s00404-009-1002-7. Epub 2009 Mar 7.

Abstract

Objective: To evaluate the maternal and fetal outcome in pregnant women with sickle cell disease and to highlight the complications encountered during pregnancy and delivery at a university hospital in the Eastern Saudi Arabia.

Study design: A retrospective study of 255 pregnancies in 145 patients with sickle cell disease (SCD) over an 8-year-period analyzed the perinatal complications and maternal and fetal outcomes compared with a control group of 500 Saudi females with the normal hemoglobin phenotype selected randomly that matched for age, parity and delivered during the study period.

Results: The incidence of SCD was 1.3% of all deliveries with one maternal death (0.4%) and a perinatal mortality rate of 78.2/1,000 deliveries in the series. The major maternal complications in the 255 pregnancies were anemia 84.3%, sickle cell crisis 44.3% (26.6% painful and 17.7% hemolytic crises), infection 45.9%, fetal growth restriction 20.1%, preterm delivery 12.6%, and pregnancy-induced hypertension 10.6%. Blood transfusion was necessary in 34% pregnancies. Stillbirths accounted for 63% of the perinatal mortality.

Conclusions: Saudi women with SCD are at a greater risk of morbidity and mortality in pregnancy than previously reported, with a high perinatal mortality rate. Early booking, meticulous antenatal care and supervised hospital delivery will improve the maternal and fetal outcomes in these patients.

MeSH terms

  • Adult
  • Anemia / pathology
  • Anemia, Sickle Cell / pathology*
  • Birth Weight
  • Female
  • Fetal Growth Retardation / pathology
  • Humans
  • Hypertension, Pregnancy-Induced / pathology
  • Infant, Newborn
  • Obstetric Labor, Premature / pathology
  • Pregnancy
  • Pregnancy Complications, Hematologic / pathology*
  • Pregnancy Outcome
  • Prenatal Care / methods
  • Retrospective Studies
  • Saudi Arabia
  • Young Adult